Hypoplastic Left Heart (HLH)

“Hypoplastic left heart syndrome (HLHS) is a complex congenital heart defect that occurs when the left side of the heart does not form properly. The mitral valve, the left ventricle and the aortic valve are too small, and there is not enough blood pumping through the left side of the heart
to support the rest of the body.

Related conditions include evolving HLHS, where the valve is beginning to narrow and there is concern that the baby will have HLHS by the time of birth, and borderline left heart, where multiple left-sided structures are smaller than they should be. Other variations on HLHS include hypoplastic left heart complex and fetal aortic stenosis.

Texas Children’s has extensive experience performing in-utero fetal cardiac interventions for all three conditions with some of the most successful outcomes in the nation. In fact, Texas Children’s Heart Center is rated #1 in the nation by U.S. News & World Report.” Read More


We will be adding more information in the future. Have questions or looking for guidance regarding a life-limiting diagnosis? Contact us here.

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