Porencephaly is an extremely rare cephalic disorder involving encephalomalacia.[1] It is a neurological disorder of the central nervous system characterized by cysts or cavities within the cerebral hemisphere.[2] Porencephaly was termed by Heschl in 1859 to describe a cavity in the human brain.[3] Derived from Greek roots, the word porencephaly means ‘holes in the brain’.[4] The cysts and cavities (cystic brain lesions) are more likely to be the result of destructive (encephaloclastic) cause, but can also be from abnormal development (malformative), direct damage, inflammation, or hemorrhage.[5] The cysts and cavities cause a wide range of physiological, physical, and neurological symptoms.[6] Depending on the patient, this disorder may cause only minor neurological problems, without any disruption of intelligence, while others may be severely disabled or face death before the second decade of their lives. However, this disorder is far more common within infants, and porencephaly can occur both before or after birth.[2]


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